ICD-10-CM 2027 · Q80-Q89

Other congenital malformations

Part of chapter 17, congenital malformations, deformations, chromosomal abnormalities, and genetic disorders.

About Q80-Q89

Block Q80-Q89 contains 9 categories and 82 billable codes for FY2027. This year's update added 1 and deleted 0 codes here. 1 codes are MCCs and 32 are CCs when reported as secondary diagnoses.

Q80Congenital ichthyosis

Q80.0Ichthyosis vulgaris
Q80.1X-linked ichthyosis
Q80.2Lamellar ichthyosis
Q80.3Congenital bullous ichthyosiform erythroderma
Q80.4Harlequin fetus
Q80.8Other congenital ichthyosis
Q80.9Congenital ichthyosis, unspecified

Q81Epidermolysis bullosa

Q81.0Epidermolysis bullosa simplex
Q81.1Epidermolysis bullosa letalis
Q81.2Epidermolysis bullosa dystrophica
Q81.8Other epidermolysis bullosa
Q81.9Epidermolysis bullosa, unspecified

Q82Other congenital malformations of skin

Q82.0Hereditary lymphedema
Q82.1Xeroderma pigmentosum
Q82.2Congenital cutaneous mastocytosis
Q82.3Incontinentia pigmenti
Q82.4Ectodermal dysplasia (anhidrotic)
Q82.5Congenital non-neoplastic nevus
Q82.6Congenital sacral dimple
Q82.8Other specified congenital malformations of skin
Q82.9Congenital malformation of skin, unspecified

Q83Congenital malformations of breast

Q83.0Congenital absence of breast with absent nipple
Q83.1Accessory breast
Q83.2Absent nipple
Q83.3Accessory nipple
Q83.8Other congenital malformations of breast
Q83.9Congenital malformation of breast, unspecified

Q84Other congenital malformations of integument

Q84.0Congenital alopecia
Q84.1Congenital morphological disturbances of hair, not elsewhere classified
Q84.2Other congenital malformations of hair
Q84.3Anonychia
Q84.4Congenital leukonychia
Q84.5Enlarged and hypertrophic nails
Q84.6Other congenital malformations of nails
Q84.8Other specified congenital malformations of integument
Q84.9Congenital malformation of integument, unspecified

Q85Phakomatoses, not elsewhere classified

Q85.0Neurofibromatosis (nonmalignant)
Q85.1Tuberous sclerosis
Q85.8Other phakomatoses, not elsewhere classified
Q85.9Phakomatosis, unspecified

Q86Congenital malformation syndromes due to known exogenous causes, not elsewhere classified

Q86.0Fetal alcohol syndrome (dysmorphic)
Q86.1Fetal hydantoin syndrome
Q86.2Dysmorphism due to warfarin
Q86.8Other congenital malformation syndromes due to known exogenous causes

Q87Other specified congenital malformation syndromes affecting multiple systems

Q87.0Congenital malformation syndromes predominantly affecting facial appearance
Q87.1Congenital malformation syndromes predominantly associated with short stature
Q87.2Congenital malformation syndromes predominantly involving limbs
Q87.3Congenital malformation syndromes involving early overgrowth
Q87.4Marfan syndrome
Q87.5Other congenital malformation syndromes with other skeletal changes
Q87.8Other specified congenital malformation syndromes, not elsewhere classified
Q87.ALoeys-Dietz syndrome

Q89Other congenital malformations, not elsewhere classified

Q89.0Congenital absence and malformations of spleen
Q89.1Congenital malformations of adrenal gland
Q89.2Congenital malformations of other endocrine glands
Q89.3Situs inversus
Q89.4Conjoined twins
Q89.7Multiple congenital malformations, not elsewhere classified
Q89.8Other specified congenital malformations
Q89.9Congenital malformation, unspecified